0 Total anomalous pulmonary venous connection (TAPVC)

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Total anomalous pulmonary venous connection (TAPVC), is a rare cyanotic congenital heart defect (CHD) in which all four pulmonary veins are malpositioned and make anomalous connections to the systemic venous circulation.
Types :

1. SupraCardiac 

  • Most Common 
  • Pulm. Veins join Superior Vena Cava


2. Cardiac  

  • Pulm. Veins join Coronary sinus


3. InfraCardiac 

  • Pulm. Veins join Portal Vein 
  • Most severe - because of Obstructive pulmonary venous hypertension.
  • Newborn with cyanosis.


All patients have ASD - Very important.
Without ASD there will be pulmonary circuit with no blood for systemic circuit.

MCQ point : O2 Saturation in Pulmonary artery is more than Aorta.

X-Ray features: 
1. SupraCardiac - Snowman Shaped Heart
2. InfraCardiac - Ground Glass appearance with Kerly B lines.




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